Intraoperative cardiovascular collapse in a patient with epidermolysis bullosa

Epidermolysis bullosa (EB) is an autosomal recessive disorder that can arise in the skin and mucosal membranes spontaneously or after trauma. These patients may require anesthesia due to esophageal balloon dilatation, surgical release of contracture pseudosyndactyly, or dental procedures. However, clinicians may face with particular difficulty in these patients due to the formation of bullae followed by scar and contractures on the skin and airways. Furthermore, significant cardiovascular effects may also occur intraoperatively [1–4].

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